Case Summary
- 3 mo baby girl
- Single orifice (small)
- Double barrel colostomy
- Increasing head circumference on admission – Hydrocephalus
- PMH: Was born with VACTERL
- 2-day-old female is admitted with bilious emesis, abdominal distention and failure to pass meconium.
- Birth weight was 3.5 kg.
- On physical exam she was noted to have a single perineal orifice.
- 6½-year-old female patient was referred in 1976 for extensive secondary surgery of her cloacal malformation
- Thirteen prior operations included:
- Colostomy at birth
- Bilateral loop ureterostomies
- Attempted vaginal pullthrough
- Opening of the urogenital sinus
- Suprapubic cystostomy
- Closure of the bladder neck
