Case Summary
- 10-yr-old female patient presents for evaluation.
- Her history included that he presented with a right colon perforation at 7 wk of age.
- She underwent partial colon resection and ileostomy.
- Incorrectly diagnosed with Hirschsprung disease.
- 2-year-old girl seen in 1979 with total urinary incontinence and a loop colostomy performed at birth in South America
- 3-year-old female patient referred for total urinary incontinence in March 1980, with an unusual cloacal variant
- At birth, exploration showed a short colon attached to the dome of a small bladder by its cecum with two appendices, the usual situation in cloacal exstrophy
- That was divided and exteriorized
- An ileostomy was also performed
- 17-year-old female referred in 1979 with total urinary and fecal incontinence despite multiple misdirected procedures for her basic cloacal malformation
- Severe hypertension secondary to renal scarring demanded immediate medical treatment
- 18-month-old female patient referred with total urinary incontinence
- Prior colostomy at birth
- Soave type rectal pullthrough at 1 year, and later colostomy closure.
- 4-year-old female patient with total urinary incontinence
- Cloaca with features seen in clocal exstrophy
- Ileocolic junction originally joined bladder
- Distal colon originally joined bladder
- Distal colon originally ended blindly
- Two adjoining bladders
- After an endoscopy 2 weeks later there was reasonable outlet resistance
- 20-year-old female totally incontinent of urine and stool when referred in 1979
- Prior operations included colostomy, colon pullthrough, right nephrectomy, and a flap to enlarge the UGS opening
- She was in diapers
- 20-year-old female patient referred in 1987, with a history of surgery for cloaca and imperforate anus
- Her problems included bowel incontinence and inability to have coitus
