6½-year-old female patient was referred in 1976 for extensive secondary surgery of her cloacal malformation
Thirteen prior operations included:
Colostomy at birth
Bilateral loop ureterostomies
Attempted vaginal pullthrough
Opening of the urogenital sinus
Suprapubic cystostomy
Closure of the bladder neck
2-year-old female patient with unusual variant of cloacal anatomy
Required only marsupialization of UG Sinus and relocation of the anus and rectum
3-year-old female patient referred for total urinary incontinence in March 1980, with an unusual cloacal variant
At birth, exploration showed a short colon attached to the dome of a small bladder by its cecum with two appendices, the usual situation in cloacal exstrophy
That was divided and exteriorized
An ileostomy was also performed
2-year-old female patient referred for cloacal repair in November 1981
No prior surgery except endoscopic and radiographic assessment of her cloacal anomaly
Normal chromosome study
On catheter drainage for several months as infant
15-year-old female patient referred in 1981 for cloacal repair
Work up at birth at two University Centers concluded patient had female pseudohermaphroditism without endocrine cause
Prior surgery was cutback of UGS and laparotomy to view (normal) pelvic organs.
14-month-old female patient referred in 1993 for cloacal reconstruction
Duodenal atresia had been repaired at birth, and right transverse colostomy
There was massive reflux bilaterally
Bilateral reimplants had been done at age 3 months, but massive reflux persisted
Newborn female patient
Esophageal atresia repaired as neonate
Had cloaca
Loop sigmoid colostomy was done
Referred at age 5½ years for cloacal repair
Chronic spillover of stool from loop colostomy, filling vagina and bladder with reflux, severe renal scaring
18-month-old female patient referred with total urinary incontinence
Prior colostomy at birth
Soave type rectal pullthrough at 1 year, and later colostomy closure.
4-year-old female patient with total urinary incontinence
Cloaca with features seen in clocal exstrophy
Ileocolic junction originally joined bladder
Distal colon originally joined bladder
Distal colon originally ended blindly
Two adjoining bladders
After an endoscopy 2 weeks later there was reasonable outlet resistance
4-year-old girl sent from abroad in 1986
Right colostomy at birth
At age 4 months, posterior sagittal operation was attempted, but abandoned after the UGS was inadvertently transected
An S.P. tube was placed
8 months later, colostomy was closed and a stricture of the neourethra was opened endoscopically
Patient was sullen, unhappy, and uncommunicative when first seen